Clinical Features, Response to Treatment, and Outcomes of IgG4-Related Sclerosing Cholangitis

Background & AimsImmunoglobulin G4 sclerosing cholangitis (IgG4-SC) is a biliary tract manifestation of IgG4-related systemic disease. We investigated the demographics, clinical features at presentation, treatment response, and outcomes of IgG4-SC using data from a large-scale survey in Japan.MethodsWe performed a retrospective cohort study of 527 patients with IgG4-SC (436 female; median age, 66.2 years; range, 23–89 years) in Japan from 2000...