Immunoglobulin G4-related pleuritis - A case report.

Published on Jan 1, 2016in Respiratory medicine case reports
· DOI :10.1016/J.RMCR.2016.05.006
Marta E. Gajewska3
Estimated H-index: 3
(Aarhus University Hospital),
Beata Agnieszka Rychwicka-Kielek1
Estimated H-index: 1
(AAU: Aalborg University)
+ 3 AuthorsElisabeth Bendstrup26
Estimated H-index: 26
(Aarhus University Hospital)
Immunoglobulin G4-related disease (IgG4-RD) is a chronic disease that presents with inflammation and fibrosis of involved tissue. It encompasses several disorders previously described using different terms, but all disorders are characterised by IgG4-positive plasma cells and lymphocytes infiltration of tissues. We report a rare case of a 58-year-old man with IgG4-related pleural disease without other systemic manifestations. The diagnosis was based on characteristic changes on PET-CT and typical histopathology in a pleural specimen. The patient’s condition improved following immunosuppressive therapy.
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