Surgical repair of double-chambered right ventricle in adulthood.

Published on Feb 1, 2011in Asian Cardiovascular and Thoracic Annals
· DOI :10.1177/0218492310395955
Brijesh P. Kottayil8
Estimated H-index: 8
Baiju S. Dharan3
Estimated H-index: 3
+ 3 AuthorsK. Jayakumar8
Estimated H-index: 8
The aim of this study was to investigate a rare subset of adult patients with double-chambered right ventricle, pertaining to clinical presentation, rhythm disturbances, surgical approach, and results of surgical repair. A retrospective review of our records revealed that 14 adults had undergone surgical repair of double-chambered right ventricle from 1990 to 2010. Their median age was 25.5 years, and their median weight was 50 kg. Patients presented with various symptoms, the most common being dyspnea on exertion. The mean systolic pressure gradient across the obstruction was 69.8 ± 23.1 mm Hg. The most common associated anomaly was ventricular septal defect. Significant rhythm disturbances were present in 4 patients. Transatrial repair was undertaken in 5 patients, a combined transatrial and transpulmonary approach was used in 4, and a right ventriculotomy in 5. There was no mortality at a median follow-up of 5.1 years. A mild right ventricular outflow tract gradient was noted in 2 patients. Medical man...
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