Intensive care medicine

Heart defect

Surgery

Cardiology

Hypoplastic left heart syndrome

Internal medicine

Heart disease

Medicine

Fontan procedure

Norwood procedure

Perfusion

Ventricle

Pediatric Clinics of North America

Hypoplastic left heart syndrome (HLHS) is a complex form of congenital heart disease defined by anatomic and functional inadequacy of the left side of the heart with nonviability of the left ventricle to perform systemic perfusion. Lethal if not treated, a strategy for survival currently is well established, with continuing improvement in outcomes over the past 30 years. Prenatal diagnosis , good newborn care , improved surgical skills, specialized postoperative care, and unique strategies for interstage monitoring all have contributed to increasing likelihood of survival. The unique life with a single right ventricle and a Fontan circulation is a focused area of investigation.

Outcomes in Hypoplastic Left Heart Syndrome