Background/Aims: This study evaluated the clinical features of double-chambered right ventricle (DCRV) in adults. Most cases of DCRV are diagnosed and treated during childhood. Consequently, very few reports include cases in which its clinical characteristics are evident in adults. Methods: We reviewed the clinical data for 10 adult patients (age ≥ 18 years) with DCRV. Results: Electrocardiogram showed right ventricular hypertrophy in 3 DCRV patients. All cases were associated with ventricular septal defect (VSD; 7 for perimembranous, 2 for muscular outlet, and 1 for the subarterial type). Surgical correction was done for 7 DCRV patients all of whom survived operations. Their follow-up echocardiogram showed the pressure gradient in their right ventricle was significantly decreased from 69.4 ± 17.2 mmHg preoperatively to 10.2 ± 5.0 mmHg postoperatively (p < 0.05). In the short-term follow-up, there was no significant increase in the pressure gradient in the right ventricle. Conclusions: There are lots of cases of DCRV that are not diagnosed accurately in adults. In our experience, all DCRV cases had VSD and surgical correction of these cases showed excellent results. Therefore, accurate diagnosis of DCRV is necessary so that DCRV is not overlooked and operations are enabled within an appropriate time. (Korean J Intern Med 2010;25:147-153)
OBJECTIVE: By means of retrospective analysis of our institutional experience, we reviewed the clinical manifestation and outcomes of patients subsequent to surgical repair of double-chambered right ventricle. METHODS: Between 1988 and 2005, we performed surgical repair in 35 of 37 patients diagnosed with double-chambered right ventricle. The patients ranged in age from 4 to 69 years, with a mean of 21.3 years. Most presented in infancy, with initial manifestation of a short systolic murmur in 3...
Abstract We report the case of a 55-year-old woman who was admitted for exertional chest pain with dyspnea. The patient was diagnosed with an isolated double-chambered right ventricle (DCRV) without associated congenital anomalies. Most cases of DCRV are diagnosed at a young age and commonly associated with VSD; isolated DCRV in adults is extremely rare.
Patients with double-chambered right ventricle presenting with symptoms in adulthood are rare. From 1990 to 2004, 4 adults and 9 children with double-chambered right ventricle underwent surgical correction. The surgical results and clinical data of the adults were compared with those of the pediatric patients. All adult patients had dyspnea on exertion, 3 children showed growth delay but the others were asymptomatic. The mean age at operation was 44.5 ± 6.3 years in adults and 5.2 ± 1.9 years in...
Objective: To evaluate the utility of echocardiography in diagnosing double chambered right ventricle (DCRV) in adults. Design: A retrospective study. Setting: Department of Congenital Heart Diseases and Department of Cardiac Surgery, Institute of Cardiology, Warsaw, Poland. Patients: 32 patients, mean age 32.5 years, 21 female, and 11 male. Intervention: Transthoracic (TTE) and transoesophageal (TOE) echocardiographic examination in patients with suspected DCRV. Main outcome measures: Direct in...
#1José M. Oliver(Hospital Universitario La Paz)H-Index: 22
#2Ana Garrido(Hospital Universitario La Paz)H-Index: 1
Last. Sanz E(Hospital Universitario La Paz)H-Index: 3
view all 7 authors...
Abstract Objective The purpose of this study was to determine the rate of progression of midventricular obstruction in adolescents and adults with double-chambered right ventricle. Methods Clinical and echocardiographic findings in 45 patients (mean age 26 ± 6 years, range 15-44) diagnosed with double-chambered right ventricle were retrospectively analyzed. Twenty patients underwent surgical repair before the age of 15 years. The relationship between Doppler midventricular pressure gradient and ...
Last. Tomio Abe(Sapporo Medical University)H-Index: 27
view all 5 authors...
Abstract Background . We reviewed the outcomes of double-chambered right ventricle repair. Methods . Between 1969 and 1998, 40 patients underwent surgical repair of a double-chamber right ventricle. The patients ranged in age from 3 months to 52 years (mean, 12.8 ± 11.6 years). Right ventricular outflow tract pressure gradients were from 20 to 170 mm Hg (mean, 65.0 ± 38.5 mm Hg) An associated ventricular septal defect was present in 27 patients (67.5%). Four patients were older than 30 years of ...
D right ventricle (DCRV) is a rare form of congenital heart disease in which the right ventricle is divided into a high-pressure inlet portion and a low-pressure outlet portion by anomalous muscle bundles. This form of midcavitary obstruction was first described by Peacock in 1858, and since 1960 many published reports have appeared describing the pathophysiology, clinical features, diagnosis, and treatment of such an entity. However, most cases of DCRV are diagnosed and treated during childhood...
#1Doff B. McElhinney(UCSF: University of California, San Francisco)H-Index: 77
#2Kanu Chatterjee(UCSF: University of California, San Francisco)H-Index: 70
Last. V. Mohan Reddy(UCSF: University of California, San Francisco)H-Index: 59
view all 3 authors...
Abstract Background . Double-chambered right ventricle is a form of right ventricular outflow tract obstruction that develops over time, often in patients with an abnormally short distance between the moderator band and pulmonary valve. This lesion typically presents in childhood or adolescence and is often accompanied by a ventricular septal defect. Only a handful of previous cases have been described in which double-chambered right ventricle occurred in adulthood. Methods . Since 1992, three p...
Abstract Objective: Our goal was to establish the morphologic nature of the obstructive muscular lesions in double-chambered right ventricle. Methods: We based our morphologic observations on 10 normal hearts and on the surgical findings in 26 patients, aged 0.5 to 24 years, with a mean of 6.9 years (SD 5.8 years). In the normal hearts, we measured the distance from the pulmonary valve to the apex of the right ventricle and from the takeoff of the moderator band to the ventricular apex. From ang...
Abstract Objectives. We sought to determine the frequency, etiology and progressive nature of midcavity obstruction in patients after primary repair of tetralogy of Fallot (TOF). Background. Midcavity obstruction (double-chambered right ventricle [DCRV]) represents a significant portion of reoperations in patients who have had TOF repair. This group is still poorly defined. Methods. A retrospective review of clinical, echocardiographic and catheterization data for all patients with TOF who later...
During diagnostic process it is very important to conduct scrupulous interview and thorough physical examination. Properly interpreted auscultation phenomena allow for appropriate planning of further imaging studies.
Abstract Background Data on the features of double-chambered right ventricular (DCRV) in adults are limited. It is also unclear how invasive and Doppler-derived assessments of right ventricular (RV) obstruction in DCRV correlate. Methods Retrospective review of 17 adults (age ≥18 years) diagnosed with DCRV who underwent right heart catheterization at Mayo Clinic, MN between 1990 and 2021. Clinical, echocardiographic, and invasive hemodynamics were abstracted from the medical charts. Results Mean...
Discrete subaortic stenosis (DSS) is a type of left ventricular outflow tract obstruction whereas double-chambered right ventricle is a form of right ventricular outflow tract obstruction. Both of these cardiac malformations share lots of similar characteristics which classify them as acquired developmental heart diseases despite their congenital anatomical substrate. Both of them are frequently associated to ventricular septal defects. The initial stimulus in their pathogenetic process is anato...
Introduction Le ventricule droit a double chambre (VDDC) est une anomalie cardiaque dans laquelle le ventricule droit (VD) est divise en deux chambres par une bande fibro-musculaire : une chambre d’admission a haute pression, en amont de l’obstacle et une chambre d’ejection a faible pression [1] . Cette anomalie est associee dans 90 % des cas a la presence d’une communication inter-ventriculaire (CIV) [2] . Le diagnostic et la prise en charge chirurgicale sont generalement realises dans l’enfanc...
We describe a case of a 69-year-old female referred for the evaluation of exertional dyspnea, with a small membranous ventricular septal defect (VSD) and right ventricle (RV) outflow tract obstruction. Using transthoracic echo was diagnosed VSD with left to right shunting and transesophageal echo (TEE) was used to a better anatomical characterization. TEE showed a perimembranous subaortic VSD that developed a high-velocity flow in RV. Pulmonary valve appears normal and right ventricular infundib...
#1W. Thaljawi(American Board of Legal Medicine)H-Index: 1
#2M. Belhadj(American Board of Legal Medicine)H-Index: 1
Last. M. Ben Dhiab(American Board of Legal Medicine)H-Index: 1
view all 9 authors...
Abstract Isolated double-chambered right ventricle (DCRV) is a rare form of congenital heart disorder in which the right ventricle is divided into a high-pressure inlet portion and a low-pressure outlet portion by an anomalous muscle bundle. Rarely, autopsy cases describing this congenital heart disease have been reported in the world literature. We report the case of a 50-day-old male who died seven days after been suffering from fever and dyspnea. The autopsy revealed essentially an isolated d...
#1Roshanak Markley(VCU: Virginia Commonwealth University)H-Index: 6
#2Asghar Ali(VCU: Virginia Commonwealth University)H-Index: 2
Last. Ion S. Jovin(VCU: Virginia Commonwealth University)H-Index: 20
view all 5 authors...
The appropriate use of echocardiography may reduce the need for invasive diagnostic cardiac procedures. The right side of the heart has recently gained interest among cardiologists as it became clear that abnormalities of the right heart morphology and function are associated with increased morbidity and mortality. Echocardiography is easy to perform, relatively cheap, readily available and do not pose the risk of ionizing radiation. Conventional 2D and, more recently, 3D echocardiography provid...
Because the systemic and pulmonary circulations are arranged in series, the right and left ventricles of the human heart have similar stroke volumes (with only minute beat-to-beat changes). Besides propelling the same volume of blood through the corresponding circulations, the two ventricles also share common structures such as the pericardium, the interventricular septum and the coronary arteries and veins—all of which complete the dynamic and integrated picture of the human heart. However, the...
Double-chambered right ventricle (DCRV) is a rare congenital heart disease in which the right ventricle (RV) is divided into two chambers by anomalous muscle bundles. Here, we report a case of DCRV associated with subarterial ventricular septal defect (VSD) and rupture of right coronary sinus aneurysm (RCSA); the patient was diagnosed by echocardiography and later confirmed by surgical operation.