A paraganglioma in a hypertensive patient with unilateral renal hypoplasia.

Published on Jan 1, 2015in Acta Medica Okayama0.642
· DOI :10.18926/AMO/53341
Tomohiro Terasaka10
Estimated H-index: 10
(Okayama University),
Hideharu Hagiya13
Estimated H-index: 13
+ 7 AuthorsFumio Otsuka35
Estimated H-index: 35
We report the case of a 46-year-old hypertensive Japanese female with renal insufficiency related to unilateral renal hypoplasia. The patient was found to have developed paraganglioma in the retroperitoneal space over a 5-year period. Catecholamine-producing tumors are not usually recognized as conditions associated with renal hypoplasia. Our long-term observation of the patient eventually led us to the diagnosis of paraganglioma. In hypertensive patients with chronic kidney disease, not only the renin-angiotensin-aldosterone system but also catecholamine activity may be involved, particularly in the patients whose cases are complicated with unilateral renal hypoplasia.
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