Fibrosing mediastinitis presenting as pulmonary stenosis: stenting works.

Published on Jun 12, 2007in International Journal of Cardiology3.229
· DOI :10.1016/J.IJCARD.2007.01.030
Ruby Satpathy7
Estimated H-index: 7
(Creighton University),
Virginia Aguila1
Estimated H-index: 1
(Creighton University)
+ 1 AuthorsIjaz A. Khan37
Estimated H-index: 37
(UMB: University of Maryland, Baltimore)
Sources
Abstract
Abstract A rare case of fibrosing mediastinitis from histoplasmosis with extrinsic compression of the right pulmonary artery is reported. A 41-year-old patient presented with worsening symptoms of cough, fever, migratory arthralgia, chest pain, and progressive dyspnea. The pulmonary artery involvement was suspected by transthoracic echo and was confirmed by transesophageal echo, CT scan of chest, and right heart catheterization. Diagnosis of histoplasmosis was confirmed by biopsy and serological tests. Patient has been free from symptoms of pulmonary stenosis for 4 years after successful pulmonary artery stenting.
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This article describes an initial experience with stent placement in three patients with severe pulmonary artery stenosis secondary to fibrosing mediastinitis. All three patients were severely symptomatic on admission and all three were asymptomatic after treatment and remained symptom-free approximately 1 year after treatment.
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