Comprehensive diagnostic criteria for IgG4-related disease (IgG4-RD), 2011

Published on Jan 5, 2012in Modern Rheumatology2.113
· DOI :10.1007/S10165-011-0571-Z
Hisanori Umehara43
Estimated H-index: 43
(Kanazawa Medical University),
Kazuichi Okazaki68
Estimated H-index: 68
(Kansai Medical University)
+ 23 AuthorsHirotaka Ohara42
Estimated H-index: 42
(Nagoya City University)
Background IgG4-related disease (IgG4-RD) is a novel clinical disease entity characterized by elevated serum IgG4 concentration and tumefaction or tissue infiltration by IgG4+ plasma cells. Although IgG4-RD is not rare and is clinically important, its clinical diagnostic criteria have not been established. Comprehensive diagnostic criteria for IgG4-RD, including the involvement of various organs, are intended for the practical use of general physicians and nonspecialists.
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