An Adolescent with Pulmonary Hypertension Secondary to Idiopathic Fibrosing Mediastinitis: Case Report
Abstract
OZET Pulmonary hypertension is an important determinant of morbidity and mortality in many diseases, including congenital heart disease and respiratory disease. Fibrosing mediastinitis is a rare disorder caused by proliferation of acellular collagen. In fibrosing mediastinitis, clinical presentation is determined by compression to the vital mediastinal organs. Fibrosing mediastinitis may rarely lead to pulmonary veno-occlusive disease. In this...
Paper Details
Title
An Adolescent with Pulmonary Hypertension Secondary to Idiopathic Fibrosing Mediastinitis: Case Report
Published Date
Sep 1, 2012
Journal
Volume
34
Issue
3
Pages
155 - 157
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