Corneal limbal xanthogranuloma in Erdheim-Chester disease

Adult orbital xanthogranulomatous disease is a rare non-Langerhans cell histiocytic condition with 4 clinical subtypes: adult‐onset xanthogranuloma, adult‐onset asthma with periocular xanthogranuloma, necrobiotic xanthogranuloma (NBX), and Erdheim–Chester disease (ECD). We report, to our knowledge, the first case of ECD with limbal infiltration. A 52-year-old woman presented with xanthomatous cutaneous lesions around her eyes and flexural folds...