Effectiveness of pirfenidone for idiopathic pulmonary fibrosis associated with pleuroparenchymal fibroelastosis‐like lesions and nonspecific interstitial pneumonia

Background Pirfenidone treatment can slow decline in forced vital capacity (FVC) in idiopathic pulmonary fibrosis (IPF). However, its effects for usual interstitial pneumonia (UIP) with pleuroparenchymal fibroelastosis‐like lesions (UIP+PPFELL) and UIP with nonspecific interstitial pneumonia (UIP+NSIP) are unclear. Objectives The aim of study is to assess pirfenidone effectiveness for UIP+PPFELL and UIP+NSIP. Methods We retrospectively analysed...