Central Nervous System Involvement in ANCA-Associated Vasculitis: What Neurologists Need to Know

Importance: Central nervous system (CNS) involvement in anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) is one of the few neurological disorders treatable with steroid and immunosuppressant. Yet AAV remains under-recognized among neurologists due to its myriad and evolving manifestations, causing diagnostic and treatment delays. Objective: To provide a comprehensive review of the CNS involvement in AAV, including the...