Maintenance therapy in autoimmune pancreatitis: a weak light into the darkness

Published on Jun 8, 2017in Annals of Translational Medicine3.297
· DOI :10.21037/ATM.2017.07.06
Luca Frulloni58
Estimated H-index: 58
,
Nicolò de Pretis8
Estimated H-index: 8
,
Antonio Amodio13
Estimated H-index: 13
Sources
Abstract
Autoimmune pancreatitis (AIP) is a fibro-inflammatory disease of the pancreas with a postulated immune-mediated mechanism (1,2). Two different histologic subtypes have been described, type 1 and type 2 AIP (3). Type 1 AIP is a more aggressive disease in terms of recurrences and extra-pancreatic organ involvement. International consensus diagnostic criteria (ICDC) have been established to classify the disease without definitive histology (4). ICDC introduced not otherwise specified (NOS) AIP as a third subtype, if type 1 or type 2 AIP cannot be diagnosed.
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