IgG4-related disease and other causes of inflammatory meningeal disease.

Published on Sep 1, 2014in Seminars in Neurology2.034
· DOI :10.1055/S-0034-1390388
Robert Carruthers12
Estimated H-index: 12
(Brigham and Women's Hospital),
Mollie N. Carruthers15
Estimated H-index: 15
(Harvard University),
Emanuel Della-Torre25
Estimated H-index: 25
Immunoglobulin-4 (IgG4-) related disease is a newly described treatable condition that has recently expanded the differential diagnosis of inflammatory meningeal disorders. This review will discuss the main clinical and pathophysiological features of IgG4-related meningeal disease in the context of meningeal inflammatory disorders in general. Particular attention will be dedicated to the differential diagnosis and the different therapeutic approaches.
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