Pulmonary atresia with intact ventricular septum

We describe the morphologic variability in pulmonary atresia with intact ventricular septum (PAIVS) within a population-based study. An uncommon disease, PAIVS shows considerable morphologic heterogeneity. Clinical reports, based mostly on small samples of patients, may not reflect the true spectrum of pathology of this condition. We have studied the entire range of morphology in a prospective population-based study of patients over a five-year...