Simultaneous occurrence of segmental odontomaxillary dysplasia and Becker's nevus.

Published on Oct 1, 1999in Journal of Oral and Maxillofacial Surgery1.642
· DOI :10.1016/S0278-2391(99)90498-6
Anne Cale Jones20
Estimated H-index: 20
(University of Texas Health Science Center at San Antonio),
Michael J. Ford5
Estimated H-index: 5
(UF: University of Florida)
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Abstract Background and Overview Segmental odontomaxillary dysplasia (SOD) is a characteristic developmental abnormality that demonstrates posterior maxillary enlargement, dental abnormalities, altered bone trabeculation, and possible cutaneous findings. Only 62 cases have been reported in the English-language literature. Case Description The authors described 3 newly diagnosed cases of SOD, all found in the left posterior maxilla in adolescent female patients; they reviewed the literature to el...
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The clinical and radiological features of segmental odontomaxillary dysplasia (SOD) are well described but the condition is probably under recognized owing to misdiagnosis as an atypical form of regional odontodysplasia (ROD). Two cases are compared to highlight the differences between SOD and ROD. The clinical, radiographic and histological findings are compared using case reports of a 6-year-old male with SOD and a 4-year-old girl with ROD. Treatment and follow-up for these patients is describ...
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Summary Introduction Becker's nevus is a dermatological disease sometimes associated with a malformation such as hemifacial bone dysplasia. Observation A 11-year-old male patient presented with a delayed growth of the left maxillary and dental impactions. At 15 years of age, Becker's nevus appeared on the upper torso, both shoulders and cheeks. Le Fort I segmented osteotomy with an iliac bone graft was complicated because of maxillary dysplasia. Discussion The chronology of our patient's cutaneo...
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Segmental Odontomaxillary Dysplasia (SOD) is an uncommon developmental disorder of unknown etiology that causes a unilateral alteration of the maxilla associated with an abnormal growth and maturation of bone, lack of one or both premolars and delayed tooth eruption on the affected side, alteration of adjacent gingival tissue with or without facial cutaneous lesions. Radiographically is observed an irregular trabecular pattern and reduction of the maxillary sinus. There are 50 cases reported in ...
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c d l In 1987, Miles et al described 2 otherwise healthy patients, 3.5 and 15 years of age, who exhibited congenital mild facial asymmetry and unilateral enlargement of the maxillary gingiva and alveolar bone. One patient had hypoplastic teeth in the affected quadrant and missing premolars, and the other patient had hypoplasia of only the premolars. The older patient also exhibited hypertrichosis of skin in the affected area. The investigators suggested the term hemimaxillofacial dysplasia (HD) ...
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