Fibrosing mediastinitis and consequent superior vena cava syndrome - A case report

Published on Jun 13, 2012in Journal of Thoracic Disease2.046
· DOI :10.3978/J.ISSN.2072-1439.2012.01.01
Saumitra Kant1
Estimated H-index: 1
(University of Texas MD Anderson Cancer Center),
Garrett L. Walsh62
Estimated H-index: 62
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Abstract
Fibrosing mediastinitis is a rare, chronic inflammatory disease that has several implicated etiologies. We describe a case of a 41-year old woman who presented with the classic signs and symptoms of superior vena cava syndrome. Imaging revealed a diffuse infiltrative mediastinal process, which on biopsy was consistent with fibrosing mediastintis.
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Cited By6
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#1Hee Kang (Kosin University Gospel Hospital)
#2Min Jung Jung (Kosin University Gospel Hospital)
Abstract Fibrosing mediastinitis is an uncommon benign disorder in which a chronic inflammatory reaction results in diffuse fibrosis of the mediastinum, potentially compromising the airways, great vessels and other mediastinal structures. Herein we describe a progressive course of fibrosing mediastinitis in a 72-year-old man. Computed tomography images depicted a diffuse, infiltrative, soft tissue mass involving the esophagus and superior vena cava in the mediastinum. Magnetic resonance imaging ...
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Mediastinal fibrosis is a rare disease characterised by fibrous proliferation in the mediastinum. It can be idiopathic or secondary to several conditions such as infections and malignancies. Anecdotal reports have described idiopathic mediastinal fibrosis (IMF) in association with other fibro-inflammatory or autoimmune diseases. We report nine new IMF cases recently seen at our Fibro-Inflammatory Disease Clinic and reviewed the IMF cases reported in the English language literature throughout 200...
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#1Ronald Tan (UCLA Medical Center)H-Index: 1
#2Joanne Martires (UCLA Medical Center)H-Index: 2
Last. Nader Kamangar (UCLA Medical Center)H-Index: 7
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Fibrosing mediastinitis is a rare condition defined by the presence of fibrotic mediastinal infiltrates that obliterate normal fat planes. It is a late complication of a previous granulomatous infection, such as histoplasmosis or tuberculosis (TB). Due to its rarity, fibrosing mediastinitis is often under-recognized, and the clinical presentation is variable and dependent on the extent of infiltration or encasement of structures within the mediastinum. We present a case of fibrosing mediastiniti...
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#1J. Y. GaubertH-Index: 1
#2C. FalqueH-Index: 2
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