Shaji C. Menon
University of Utah
Internal medicineSurgeryCardiologyRetrospective cohort studyIntensive care medicinePediatricsEmergency medicineFontan procedureVascular surgeryCardiac surgeryVentricleHypoplastic left heart syndromeHeart diseaseHypertrophic cardiomyopathyPulmonary arteryPopulationResource utilizationMedicineCohortEjection fraction
Publications 110
#1Cathleen R. Pruitt (UofU: University of Utah)
#2Shaji C. Menon (UofU: University of Utah)H-Index: 22
Last. Mary Niu (UofU: University of Utah)H-Index: 1
view all 8 authors...
Cardiac arrhythmias occur in 3-40% of patients with acute myocarditis and cause significant morbidity and mortality. Myocardial injury also results in abnormal myocardial deformation. The relationship between left ventricular (LV) deformation, measured by two-dimensional speckle tracking echocardiography (2D-STE), and arrhythmia in pediatric myocarditis is unknown. We evaluated the association between 2D-STE and arrhythmias in children hospitalized with acute myocarditis. We reviewed patients ≤ ...
#1Lindsey Gakenheimer-Smith (UofU: University of Utah)H-Index: 2
#2Lindsay MeyersH-Index: 9
Last. Susan P. Etheridge (UofU: University of Utah)H-Index: 35
view all 8 authors...
Background Pathogenic variants in the L-type Ca2+ channel gene CACNA1C cause a multi-system disorder that includes severe long QT syndrome (LQTS), congenital heart disease, dysmorphic facial features, syndactyly, abnormal immune function, and neuropsychiatric disorders, collectively known as Timothy syndrome. In 2015, a variant in CACNA1C (p.R518C) was reported to cause cardiac-only Timothy syndrome, a genetic disorder with a mixed phenotype of congenital heart disease, hypertrophic cardiomyopat...
#1Michael V. Di MariaH-Index: 11
#2David J. GoldbergH-Index: 28
Last. Peter C. FrommeltH-Index: 37
view all 35 authors...
Introduction: The Pediatric Heart Network’s Fontan Udenafil Exercise Longitudinal (FUEL) Trial (Mezzion Pharma Co. Ltd., NCT 02741115) demonstrated improvements in exercise capacity following 6 mon...
#1D. K. Singh (UofU: University of Utah)H-Index: 6
#2Shaji C. Menon (UofU: University of Utah)H-Index: 22
Last. Michael D. Puchalski (Primary Children's Hospital)H-Index: 21
view all 3 authors...
BACKGROUND: In Fontan circulation, ventricular filling is dependent on active atrial contraction. This atrioventricular interdependence is key for optimal exercise performance. The objectives of this study were to evaluate the relationship between atrial and ventricular deformation in young Fontan survivors and their relationship to exercise performance (peak oxygen consumption; VO2 max). METHODS: Single center retrospective cohort study …
#1Kevin Hummel (UofU: University of Utah)H-Index: 2
#2Kristi Glotzbach (UofU: University of Utah)H-Index: 1
Last. Ashwin K. Lal (UofU: University of Utah)H-Index: 9
view all 5 authors...
This case describes an uncommon acute complication of diffuse thrombotic angiopathy and associated aHUS/TTP in an 11-year-old girl with Danon disease who underwent orthotopic heart transplant. Shortly after transplant, despite an uncomplicated operative course, the patient developed severe kidney injury and progressive altered mental status, culminating in cerebral edema, brain herniation, and death. She had received a single dose of tacrolimus (FK506) and a single dose of antithymocyte globulin...
1 CitationsSource
#1Linda M. Lambert (Primary Children's Hospital)H-Index: 24
#2Brian W. McCrindleH-Index: 114
Last. Shaji C. Menon (Primary Children's Hospital)H-Index: 22
view all 12 authors...
Abstract Background Growth abnormalities in single ventricle survivors may reduce quality of life (QoL) and exercise capacity. Methods This multicenter, longitudinal analysis evaluated changes in height and body mass index (BMI) compared to population norms and their relationship to mortality, ventricular morphology, QoL, and exercise capacity in the Pediatric Heart Network (PHN) Fontan studies. Results Fontan1 (F1) included 546 participants (12 ± 3.4 yrs.), Fontan 2 (F2) 427 (19 ± 3.4 yrs.), an...
#1David J. Goldberg (Children's Hospital of Philadelphia)H-Index: 28
#2Victor ZakH-Index: 17
Last. Stephen M. Paridon (Children's Hospital of Philadelphia)H-Index: 42
view all 42 authors...
Background: The Fontan operation creates a total cavopulmonary connection, a circulation in which the importance of pulmonary vascular resistance is magnified. Over time, this circulation leads to ...
33 CitationsSource
#1Andrew B. Goldstone (Children's Hospital of Philadelphia)H-Index: 1
#2Michael Baiocchi (Stanford University)H-Index: 15
Last. J. William Gaynor (Children's Hospital of Philadelphia)H-Index: 93
view all 29 authors...
OBJECTIVES: Neurodevelopmental disability is the most common complication among congenital heart surgery survivors. The Bayley scales are standardized instruments to assess neurodevelopment. The most recent edition (Bayley Scales of Infant and Toddler Development 3rd Edition, Bayley-III) yields better-than-expected scores in typically developing and high-risk infants than the second edition (Bayley Scales of Infant Development 2nd Edition, BSID-II). We compared BSID-II and Bayley-III scores in i...
2 CitationsSource
Ebstein anomaly (EA) is often considered just a tricuspid valve (TV) disease. However, left heart lesions are not infrequent, and portend poor prognosis with serious clinical implications. A 5 year-old female presented to ER with syncope and murmur. Echo revealed EA of TV with mild TR, a large